Exterior Wood Stain | Wolman - Rust-Oleum
网页Wolman exterior wood stains, sealers, cleaners, brighteners and removers protect and enhance the beauty of wooden decks, fences, siding and outdoor furniture. The long-lasting exterior wood stains provide superior water repellency, UV resistance and lasting protection. Choose from clear wood stain and rich-colored semi-transparent and solid ...
Wood protection | Wolman
网页Our products offer protection against wood-destroying fungi and insects, extend the life of the wood and thus increase its sustainable use. Founded in 1911, we can look back on over a century of experience in the preservation of timber.
Wolman Disease - Symptoms, Causes, Treatment | NORD
网页2016年8月15日 · Wolman disease is a type of lysosomal acid lipase (LAL) deficiency; a rare genetic disorder characterized by complete absence of an enzyme known as lysosomal acid lipase (LIPA or LAL). This enzyme is required to breakdown (metabolize) certain fats …
胆固醇酯沉积症和Wolman病 - 胆固醇酯沉积症和Wolman病
网页胆固醇酯沉积症和沃尔曼病是一种遗传性代谢紊乱、溶酶体酸酯酶缺陷引起的 神经类脂增多症，导致高脂血症和肝肿大。. 欲了解更多信息，见表神经鞘脂贮积症和其他脂质沉积。. 也可参见可疑遗传性代谢病的诊断程序。. 这两种病是罕见的常染色体隐性遗传病 ...
Wolman disease | About the Disease | GARD - Genetic and Rare …
网页Wolman disease is a congenital disease characterized by an impaired metabolism of the fats (lipids). It is the most severe type of lysosomal acid lipase deficiency. The lysomal acid lipase deficiency causes a buildup of lipids (fats) in …
High-Dose ERT, Rituximab, and Early HSCT in an Infant with Wolman…
网页2024年2月14日 · Wolman’s disease, a severe form of lysosomal acid lipase deficiency, leads to pathologic lipid accumulation in the liver and gut that, without treatment, is fatal in infancy.
沃尔曼病 - 百度百科
网页沃尔曼(Wolman)病 (胆固醇酯水解酶缺乏) 常染色体隐性遗传,特征是肝,脾肿大,腹胀及在生后1周内出现肾上腺钙化.
Wolman 5 Gal. F&P Natural Exterior Wood Stain Finish and Preservative ...
网页Wolman F&P Natural Exterior Wood Stain Finish and Preservative keeps your wood protected. Perfect for fences, decks and siding, this stain covers up to 200 sq. ft. It produces a rich oil finish and offers moisture and UV resistance for lasting use.
Diagnosis, treatment, and follow-up of a case of Wolman disease …
网页2021年12月20日 · Wolman Disease (WD) is a severe multi-system metabolic disease due to lysosomal acid lipase (LAL) deficiency. We report on a WD infant who developed an unusual hemophagocytic lymphohistiocytosis (HLH) phenotype related to …
Wolman - Consumer Group | RPM International Inc.
网页The Wolman brand includes water-repellent coatings, stains and removers for the restoration and protection of outdoor wood finishes, including decks, furniture and décor, fences, play sets and siding. Among its leading products are DuraStain solid color stain, RainCoat water-based clear sealer and DeckBrite wood cleaner and coating prep.